DB96

ICD-11 MMS 2026-01

Autoimmune liver disease

Description

Autoimmune liver diseases are generally forms of chronic liver disease in which the etiology is unclear but autoimmune mechanisms are evident or postulated for the development of the disease. The primary target organ is the liver and/or biliary system. It can progress to liver cirrhosis.

Exclusions from above levels

  • ME10.1 – Unspecified jaundice
  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • DB96.0 – Autoimmune hepatitis
  • DB96.1 – Primary biliary cholangitis
  • DB96.2 – Primary sclerosing cholangitis
  • DB96.Y – Other specified autoimmune liver disease
  • DB96.Z – Autoimmune liver disease, unspecified

Sibling codes

  • DB90 – Infectious liver disease
  • DB91 – Acute or subacute hepatic failure
  • DB92 – Non-alcoholic fatty liver disease
  • DB93 – Hepatic fibrosis or cirrhosis
  • DB94 – Alcoholic liver disease
  • DB95 – Drug-induced or toxic liver disease
  • DB97 – Certain specified inflammatory liver diseases
  • DB98 – Vascular disorders of the liver
  • DB99 – Certain specified diseases of liver
  • DB9Z – Diseases of liver, unspecified

Foundation entity

Autoimmune liver disease – http://id.who.int/icd/entity/1057142191

Allowed postcoordination axes

Part of: 13: Diseases of the digestive system