DB96.0

ICD-11 MMS 2026-01

Autoimmune hepatitis

Description

Autoimmune hepatitis is a chronic hepatitis, which can progress to liver cirrhosis, generally featured by the presence of circulating autoantibodies and hyperglobulinemia. It has been subdivided into three main categories according to the autoantibodies detected.

Index terms

  • Autoimmune hepatitis
  • Autoantibody negative autoimmune hepatitis
  • Autoimmune hepatitis type 1
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  • Autoimmune hepatitis type 1 with cirrhosis
  • Autoimmune hepatitis type 1 with cirrhosis, with cirrhosis-related complications
  • Autoimmune hepatitis type 1 with cirrhosis, without cirrhosis-related complications
  • Autoimmune hepatitis type 1 without cirrhosis
  • Autoimmune hepatitis type 1 NEC
  • Autoimmune hepatitis type 2
  • Autoimmune hepatitis type 2 with cirrhosis
  • Autoimmune hepatitis type 2 with cirrhosis, with cirrhosis-related complications
  • Autoimmune hepatitis type 2 with cirrhosis, without cirrhosis-related complications
  • Autoimmune hepatitis type 2 without cirrhosis
  • Autoimmune hepatitis type 3
  • Autoimmune hepatitis type 3 with cirrhosis
  • Autoimmune hepatitis type 3 with cirrhosis, with cirrhosis-related complications
  • Autoimmune hepatitis type 3 with cirrhosis, without cirrhosis-related complications
  • Autoimmune hepatitis type 3 without cirrhosis
  • Autoimmune hepatitis type 3 NEC
  • Autoimmune hepatitis type 3 without mention of cirrhosis
  • Autoimmune hepatitis with cholestasis
  • Autoimmune cholangitis
  • Autoimmune chronic active hepatitis

Exclusions from above levels

  • ME10.1 – Unspecified jaundice
  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • DB96.1 – Primary biliary cholangitis
  • DB96.2 – Primary sclerosing cholangitis
  • DB96.Y – Other specified autoimmune liver disease
  • DB96.Z – Autoimmune liver disease, unspecified

Foundation entity

Autoimmune hepatitis – http://id.who.int/icd/entity/1235727122

Allowed postcoordination axes

Part of: DB96: Autoimmune liver disease › 13: Diseases of the digestive system