DB96.2

ICD-11 MMS 2026-01

Primary sclerosing cholangitis

Description

Primary sclerosing cholangitis is a chronic disease which shows focal or multifocal strictures of intra- and/or extra-hepatic bile ducts without any apparent causes, leading to cholestasis and ultimately liver cirrhosis and liver failure.

Exclusions from above levels

  • ME10.1 – Unspecified jaundice
  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • DB96.20 – Primary sclerosing cholangitis with cirrhosis
  • DB96.2Y – Other specified primary sclerosing cholangitis
  • DB96.2Z – Primary sclerosing cholangitis, unspecified

Sibling codes

  • DB96.0 – Autoimmune hepatitis
  • DB96.1 – Primary biliary cholangitis
  • DB96.Y – Other specified autoimmune liver disease
  • DB96.Z – Autoimmune liver disease, unspecified

Foundation entity

Primary sclerosing cholangitis – http://id.who.int/icd/entity/857962451

Allowed postcoordination axes

Part of: DB96: Autoimmune liver disease › 13: Diseases of the digestive system