FA24.2

ICD-11 MMS 2026-01

Juvenile psoriatic arthritis

Description

Juvenile psoriatic arthritis is an autoimmune inflammatory disorder representing less than 10% of all juvenile idiopathic arthritis (JIA) cases, and characterised by the association of psoriasis with one of two forms of arthritis: the association of psoriasis with an arthritis that most resembles oligoarticular arthritis with a risk of uveitis is more common in girls with onset at around 6 years of age, whereas the association of psoriasis with a form of arthritis that most resembles a spondyloarthropathy is most common in boys and manifests later.

Coding note

Use additional code to identify associated uveitis

Coding note from above levels

Arthritis in children, with onset before 16th birthday and lasting longer than 6 weeks

Index terms

  • Juvenile psoriatic arthritis
  • Juvenile psoriatic arthritis, ANA negative
  • Juvenile psoriatic arthritis, ANA negative, with uveitis
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  • Juvenile psoriatic arthritis, rheumatoid factor negative, HLA B27 negative
  • Juvenile psoriatic arthritis, rheumatoid factor positive, HLA B27 negative
  • Juvenile psoriatic arthritis, rheumatoid factor positive, HLA B27 positive
  • Juvenile psoriatic arthritis, rheumatoid factor negative, HLA B27 positive
  • Juvenile psoriatic arthritis, ANA positive
  • Juvenile psoriatic arthritis, ANA positive, with uveitis
  • Juvenile psoriatic arthritis, multiple sites
  • juvenile arthritis in psoriasis, multiple sites
  • Juvenile psoriatic arthritis, shoulder region
  • juvenile arthritis in psoriasis, shoulder region
  • Juvenile psoriatic arthritis, acromioclavicular joint
  • Juvenile psoriatic arthritis, glenohumeral joint
  • Juvenile psoriatic arthritis, sternoclavicular joint
  • Juvenile psoriatic arthritis, upper arm
  • juvenile arthritis in psoriasis, upper arm
  • Juvenile psoriatic arthritis, elbow joint
  • Juvenile psoriatic arthritis, forearm
  • juvenile arthritis in psoriasis, forearm
  • Juvenile psoriatic arthritis, wrist joint
  • juvenile arthritis in psoriasis, wrist joint
  • Juvenile psoriatic arthritis, hand
  • juvenile arthritis in psoriasis, hand
  • Juvenile psoriatic arthritis, carpus
  • Juvenile psoriatic arthritis, fingers
  • Juvenile psoriatic arthritis, metacarpus
  • Juvenile psoriatic arthritis, pelvic region or thigh
  • juvenile arthritis in psoriasis, pelvic region or thigh
  • Juvenile psoriatic arthritis, hip joint
  • Juvenile psoriatic arthritis, lower leg
  • juvenile arthritis in psoriasis, lower leg
  • Juvenile psoriatic arthritis, knee joint
  • Juvenile psoriatic arthritis, ankle or foot
  • juvenile arthritis in psoriasis, ankle or foot
  • Juvenile psoriatic arthritis, metatarsus
  • Juvenile psoriatic arthritis, tarsus
  • Juvenile psoriatic arthritis, toes
  • Juvenile psoriatic arthritis, ankle joint
  • Juvenile psoriatic arthritis, other joints in foot
  • Juvenile psoriatic arthritis, head
  • Juvenile psoriatic arthritis, neck
  • Juvenile psoriatic arthritis, vertebral column

Exclusions from above levels

  • 4A41.01 – Juvenile dermatomyositis
  • FA20.0 – Felty syndrome
  • 01 – Certain infectious or parasitic diseases
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • DA0E.8 – Temporomandibular joint disorders

Sibling codes

  • FA24.0 – Juvenile idiopathic oligoarthritis
  • FA24.1 – Juvenile idiopathic polyarthritis
  • FA24.3 – Juvenile enthesitis related arthritis
  • FA24.4 – Juvenile systemic arthritis
  • FA24.Y – Other specified juvenile idiopathic arthritis
  • FA24.Z – Juvenile idiopathic arthritis, unspecified

Foundation entity

Juvenile psoriatic arthritis – http://id.who.int/icd/entity/1473955563

Allowed postcoordination axes

Part of: FA24: Juvenile idiopathic arthritis › 15: Diseases of the musculoskeletal system or connective tissue