FA24.3

ICD-11 MMS 2026-01

Juvenile enthesitis related arthritis

Description

Enthesitis-related arthritis is a type of juvenile idiopathic arthritis (JIA) that represents the paediatric form of spondyloarthropathy in adults, but differs from it as the initial manifestations in the paediatric form are asymmetric oligoarticular arthritis of the lower limbs, associated with enthesitis. Axial manifestations (sacroiliac involvement) are present in only 25% of cases at onset but appear several years later in the disease course.

Coding note

Use additional code to identify associated uveitis

Coding note from above levels

Arthritis in children, with onset before 16th birthday and lasting longer than 6 weeks

Index terms

  • Juvenile enthesitis related arthritis
  • Juvenile enthesitis related arthritis, ANA positive
  • Juvenile enthesitis related arthritis, ANA positive, with uveitis
Show allHide
  • Juvenile enthesitis related arthritis, ANA negative
  • Juvenile enthesitis related arthritis, ANA negative, with uveitis
  • Juvenile enthesitis related arthritis, HLA B27 negative
  • Juvenile enthesitis related arthritis, HLA B27 negative, with uveitis
  • Juvenile enthesitis related arthritis, HLA B27 positive
  • Juvenile enthesitis related arthritis, HLA B27 positive, with uveitis

Exclusions from above levels

  • 4A41.01 – Juvenile dermatomyositis
  • FA20.0 – Felty syndrome
  • 01 – Certain infectious or parasitic diseases
Show allHide
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • DA0E.8 – Temporomandibular joint disorders

Sibling codes

  • FA24.0 – Juvenile idiopathic oligoarthritis
  • FA24.1 – Juvenile idiopathic polyarthritis
  • FA24.2 – Juvenile psoriatic arthritis
  • FA24.4 – Juvenile systemic arthritis
  • FA24.Y – Other specified juvenile idiopathic arthritis
  • FA24.Z – Juvenile idiopathic arthritis, unspecified

Foundation entity

Juvenile enthesitis related arthritis – http://id.who.int/icd/entity/1128255226

Allowed postcoordination axes

Part of: FA24: Juvenile idiopathic arthritis › 15: Diseases of the musculoskeletal system or connective tissue