Congenital hydrocephalus

Description

A disease caused by failure of the brain to correctly develop during the antenatal period. This condition is characterised by a rapid increase in head circumference or an unusually large head size due to excessive accumulation of cerebrospinal fluid in the brain. This condition may also present with vomiting, sleepiness, irritability, downward deviation of the eyes, or seizures. Confirmation is through observation of cerebrospinal fluid within cerebral ventricles by imaging.

Inclusions

Hydrocephalus in newborn

Excludes

KA64.0 – Hydrocephalus due to congenital toxoplasmosis
LA02.00 – Myelomeningocele with hydrocephalus
LA03 – Arnold-Chiari malformation type II
LA07.4 – Arnold-Chiari malformation type I

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Child codes

LA04.0 – Hydrocephalus with stenosis of the aqueduct of Sylvius
LA04.Y – Other specified congenital hydrocephalus
LA04.Z – Congenital hydrocephalus, unspecified

Sibling codes

LA00 – Anencephaly or similar anomalies
LA01 – Cephalocele
LA02 – Spina bifida
LA03 – Arnold-Chiari malformation type II
LA05 – Cerebral structural developmental anomalies
LA06 – Cerebellar structural developmental anomalies
LA07 – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
LA0Y – Other specified structural developmental anomalies of the nervous system
LA0Z – Structural developmental anomalies of the nervous system, unspecified

Foundation entity

Congenital hydrocephalus – http://id.who.int/icd/entity/1878746673

Part of: 20: Developmental anomalies