Primary tethered cord syndrome

Description

A condition caused by failure of the spinal cord to correctly develop during the antenatal period. This condition is characterised by tethering of the spinal cord to the spinal canal. This condition may present with lower back skin appendages, radicular pain, weakness, asymmetric hyporeflexia, spasticity, sensory changes, bowel or bladder dysfunction, or motor dysfunction. Confirmation is through observation of a tethered spinal cord by imaging.

Index terms

Primary tethered cord syndrome

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA07.1 – Diastematomyelia
LA07.2 – Amyelia
LA07.3 – Primary syringomyelia or hydromyelia
LA07.4 – Arnold-Chiari malformation type I
LA07.Y – Other specified structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
LA07.Z – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column, unspecified

Foundation entity

Primary tethered cord syndrome – http://id.who.int/icd/entity/66705662

Allowed postcoordination axes

hasManifestation

Part of: LA07: Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column › 20: Developmental anomalies