LA07.1

ICD-11 MMS 2026-01

Diastematomyelia

Description

A condition caused by failure of the spinal cord during the antenatal period. This condition is characterised by separation of the spinal cord into two parts by a rigid or fibrous septum. This condition may present with misformed vertebrae, pain, weakness, impaired gait, sensory changes in the legs, or sphincter disturbance. Confirmation is through observation of a septum-bifurcated spinal cord by imaging.

Index terms

  • Diastematomyelia
  • Split cord malformation
  • diplomyelia

Inclusions

  • Split cord malformation

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA07.0 – Primary tethered cord syndrome
  • LA07.2 – Amyelia
  • LA07.3 – Primary syringomyelia or hydromyelia
  • LA07.4 – Arnold-Chiari malformation type I
  • LA07.Y – Other specified structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
  • LA07.Z – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column, unspecified

Foundation entity

Diastematomyelia – http://id.who.int/icd/entity/2070601288

Allowed postcoordination axes

Part of: LA07: Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column › 20: Developmental anomalies