LA90.10

ICD-11 MMS 2026-01

Macrocystic lymphatic malformation

Description

A condition caused by failure of the lymphatic system to correctly develop during the antenatal period. This condition is characterised by large, soft, smooth clear masses under normal or bluish skin. This condition may be associated with cellulitis, bleeding within the malformation, pain, or leakage of lymphatic fluid internally.

Index terms

  • Macrocystic lymphatic malformation
  • Cavernous lymphangioma
  • Cavernous lymphatic malformation
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  • Macrocystic lymphangioma
  • Circumscribed lymphatic malformation
  • Circumscribed lymphangioma
  • Lymphangiomatous cyst of unspecified site

Exclusions from above levels

  • 2E81 – haemangioma and lymphangioma
  • LA13.5 – Congenital retinal aneurysm
  • LA8B.1 – Congenital anomaly of pulmonary arterial tree
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  • LA8C – Congenital anomaly of coronary artery
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA90.11 – Microcystic lymphatic malformation
  • LA90.12 – Lymphatic malformations of certain specified sites
  • LA90.13 – Cystic hygroma in fetus
  • LA90.1Y – Other specified lymphatic malformations
  • LA90.1Z – Lymphatic malformations, unspecified

Foundation entity

Macrocystic lymphatic malformation – http://id.who.int/icd/entity/1525487462

Allowed postcoordination axes

Part of: LA90.1: Lymphatic malformations › LA90: Structural developmental anomalies of the peripheral vascular system › 20: Developmental anomalies