LA90.11

ICD-11 MMS 2026-01

Microcystic lymphatic malformation

Description

Microcystic lymphatic malformations consist of clusters of dilated lymphatic vessels which have developed without connection to the systemic lymphatic circulation. They present with grouped clear or haemorrhagic vesicles anywhere on the skin or mucous membrane.

Index terms

  • Microcystic lymphatic malformation
  • Capillary lymphangioma
  • Capillary lymphatic malformation
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  • Lymphangioma circumscriptum
  • Microcystic infiltrating lymphatic malformation
  • Microcystic lymphangioma
  • Superficial lymphangioma

Inclusions

  • Lymphangioma circumscriptum

Excludes

  • LA90.10 – Circumscribed lymphatic malformation

Exclusions from above levels

  • 2E81 – haemangioma and lymphangioma
  • LA13.5 – Congenital retinal aneurysm
  • LA8B.1 – Congenital anomaly of pulmonary arterial tree
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  • LA8C – Congenital anomaly of coronary artery
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA90.10 – Macrocystic lymphatic malformation
  • LA90.12 – Lymphatic malformations of certain specified sites
  • LA90.13 – Cystic hygroma in fetus
  • LA90.1Y – Other specified lymphatic malformations
  • LA90.1Z – Lymphatic malformations, unspecified

Foundation entity

Microcystic lymphatic malformation – http://id.who.int/icd/entity/1796778763

Allowed postcoordination axes

Part of: LA90.1: Lymphatic malformations › LA90: Structural developmental anomalies of the peripheral vascular system › 20: Developmental anomalies