LB30.1

ICD-11 MMS 2026-01

Renal dysplasia

Description

A condition characterised by abnormal development of one or both kidneys.

Index terms

  • Renal dysplasia
  • congenital renal dysplasia
  • dysplasia of kidney
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  • dysplastic kidney
  • Primary renal dysplasia
  • Primary renal dysplasia, unilateral
  • unilateral renal dysplasia
  • Primary renal dysplasia, bilateral
  • Bilateral renal dysplasia
  • Secondary renal dysplasia
  • Secondary renal dysplasia, unilateral
  • Secondary renal dysplasia, bilateral

Excludes

  • GB81 – Autosomal dominant polycystic kidney disease

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB30.0 – Renal agenesis or other reduction defects of kidney
  • LB30.2 – Congenital single renal cyst
  • LB30.3 – Renal tubular dysgenesis
  • LB30.4 – Oligomeganephronia
  • LB30.5 – Accessory kidney
  • LB30.6 – Fusion anomaly of kidneys
  • LB30.7 – Ectopic or pelvic kidney
  • LB30.8 – Medullary sponge kidney
  • LB30.9 – Multicystic renal dysplasia
  • LB30.Y – Other specified structural developmental anomalies of kidneys
  • LB30.Z – Structural developmental anomalies of kidneys, unspecified

Foundation entity

Renal dysplasia – http://id.who.int/icd/entity/921320354

Allowed postcoordination axes

Part of: LB30: Structural developmental anomalies of kidneys › 20: Developmental anomalies