LB30.8

ICD-11 MMS 2026-01

Medullary sponge kidney

Description

A condition characterised by cystic or saccular dilatations of the medullary collecting ducts seen with radiocontrast filling. A predisposition to stones and associated often with renal tubular acidosis. There is no clear genetic predisposition.

Index terms

  • Medullary sponge kidney
  • Cacchi-Ricci disease
  • MSK - [medullary sponge kidney]
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  • sponge kidney NOS
  • Medullary sponge kidney, unilateral
  • Medullary sponge kidney, bilateral

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB30.0 – Renal agenesis or other reduction defects of kidney
  • LB30.1 – Renal dysplasia
  • LB30.2 – Congenital single renal cyst
  • LB30.3 – Renal tubular dysgenesis
  • LB30.4 – Oligomeganephronia
  • LB30.5 – Accessory kidney
  • LB30.6 – Fusion anomaly of kidneys
  • LB30.7 – Ectopic or pelvic kidney
  • LB30.9 – Multicystic renal dysplasia
  • LB30.Y – Other specified structural developmental anomalies of kidneys
  • LB30.Z – Structural developmental anomalies of kidneys, unspecified

Foundation entity

Medullary sponge kidney – http://id.who.int/icd/entity/1723148250

Allowed postcoordination axes

Part of: LB30: Structural developmental anomalies of kidneys › 20: Developmental anomalies