LB30.4

ICD-11 MMS 2026-01

Oligomeganephronia

Description

Oligomeganephronic renal hypoplasia is a severe developmental defect of both kidneys characterised by a reduced number of nephrons (the functional unit of the kidney), hypertrophic glomeruli with diameters twice the normal size, hypertrophic tubules and thickening of Bowman's capsule, occurring in the absence of a urinary tract malformation.

Index terms

  • Oligomeganephronia

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB30.0 – Renal agenesis or other reduction defects of kidney
  • LB30.1 – Renal dysplasia
  • LB30.2 – Congenital single renal cyst
  • LB30.3 – Renal tubular dysgenesis
  • LB30.5 – Accessory kidney
  • LB30.6 – Fusion anomaly of kidneys
  • LB30.7 – Ectopic or pelvic kidney
  • LB30.8 – Medullary sponge kidney
  • LB30.9 – Multicystic renal dysplasia
  • LB30.Y – Other specified structural developmental anomalies of kidneys
  • LB30.Z – Structural developmental anomalies of kidneys, unspecified

Foundation entity

Oligomeganephronia – http://id.who.int/icd/entity/1283447040

Allowed postcoordination axes

Part of: LB30: Structural developmental anomalies of kidneys › 20: Developmental anomalies