LB30.9

ICD-11 MMS 2026-01

Multicystic renal dysplasia

Description

Multicystic renal dysplasia, or multicystic dysplastic kidney (MCDK), is a congenital condition where a kidney fails to develop properly in the womb, becoming a non-functional collection of fluid-filled cysts instead of normal kidney tissue. It most often affects a single kidney, allowing the other healthy kidney to compensate for its function, and is usually discovered via prenatal ultrasound. Bilateral MCDK, affecting both kidneys, is a very serious condition with a high risk of kidney failure and is often incompatible with long-term survival.

Index terms

  • Multicystic renal dysplasia
  • MCDK - [multicystic dysplastic kidney]
  • developmental multicystic kidney
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  • multicystic dysplastic kidney
  • multiple congenital cysts of kidney
  • Multicystic renal dysplasia, unilateral
  • Unilateral multicystic dysplastic kidney
  • Multicystic renal dysplasia, bilateral

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB30.0 – Renal agenesis or other reduction defects of kidney
  • LB30.1 – Renal dysplasia
  • LB30.2 – Congenital single renal cyst
  • LB30.3 – Renal tubular dysgenesis
  • LB30.4 – Oligomeganephronia
  • LB30.5 – Accessory kidney
  • LB30.6 – Fusion anomaly of kidneys
  • LB30.7 – Ectopic or pelvic kidney
  • LB30.8 – Medullary sponge kidney
  • LB30.Y – Other specified structural developmental anomalies of kidneys
  • LB30.Z – Structural developmental anomalies of kidneys, unspecified

Foundation entity

Multicystic renal dysplasia – http://id.who.int/icd/entity/1178642763

Allowed postcoordination axes

Part of: LB30: Structural developmental anomalies of kidneys › 20: Developmental anomalies