2A81.0ICD-11 MMS 2026-01
Primary mediastinal large B-cell lymphoma
Description
A large B-cell non-Hodgkin lymphoma arising in the mediastinum. Morphologically it is characterised by a massive diffuse lymphocytic proliferation associated with compartmentalizing fibrosis.
Index terms
- Primary mediastinal large B-cell lymphoma
- Mediastinal large B-cell lymphoma
- Mediastinal diffuse large-cell lymphoma with sclerosis
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- Mediastinal thymic large B-cell lymphoma
Exclusions from above levels
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Sibling codes
2A81.1– Intravascular large B-cell lymphoma2A81.2– Plasmablastic lymphoma2A81.3– Lymphomatoid granulomatosis2A81.4– T-cell/histiocyte rich large B-cell lymphoma2A81.5– Primary diffuse large B-cell lymphoma of central nervous system2A81.6– Epstein-Barr Virus-positive diffuse large B-cell lymphoma of the elderly2A81.7– Diffuse large B-cell lymphoma associated with chronic inflammation2A81.8– ALK-positive large B-cell lymphoma2A81.9– Primary effusion lymphoma2A81.A– Primary cutaneous diffuse large B-cell lymphoma, leg type2A81.Y– Other specified diffuse large B-cell lymphomas2A81.Z– Diffuse large B-cell lymphoma, not otherwise specified
Foundation entity
Primary mediastinal large B-cell lymphoma – http://id.who.int/icd/entity/950282079
Allowed postcoordination axes
Part of: 2A81: Diffuse large B-cell lymphomas › 02: Neoplasms