2A90.0

ICD-11 MMS 2026-01

T-cell prolymphocytic leukaemia

Description

An aggressive T-cell leukaemia, characterised by the proliferation of small to medium sized prolymphocytes with a mature T-cell phenotype, involving the blood, bone marrow, lymph nodes, liver, spleen, and skin.

Index terms

  • T-cell prolymphocytic leukaemia
  • prolymphocytic leukaemia of T-cell type without mention of remission
  • T-cell prolymphocytic leukaemia in complete remission
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  • prolymphocytic leukaemia of T-cell type in complete remission

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A90.1 – T-cell large granular lymphocytic leukaemia
  • 2A90.2 – Chronic lymphoproliferative disorders of NK-cells
  • 2A90.3 – Aggressive NK cell leukaemia
  • 2A90.4 – Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood
  • 2A90.5 – Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
  • 2A90.6 – Extranodal NK/T-cell lymphoma, nasal type
  • 2A90.7 – Enteropathy associated T-cell lymphoma
  • 2A90.8 – Hepatosplenic T-cell lymphoma
  • 2A90.9 – Angioimmunoblastic T-cell lymphoma
  • 2A90.A – Anaplastic large cell lymphoma, ALK-positive
  • 2A90.B – Anaplastic large cell lymphoma, ALK-negative
  • 2A90.C – Peripheral T-cell lymphoma, not otherwise specified

Foundation entity

T-cell prolymphocytic leukaemia – http://id.who.int/icd/entity/352523899

Allowed postcoordination axes

Part of: 2A90: Mature T-cell lymphoma, specified types, nodal or systemic › 02: Neoplasms