2A90.7

ICD-11 MMS 2026-01

Enteropathy associated T-cell lymphoma

Description

An uncommon mature T-cell lymphoma of intraepithelial lymphocytes. It usually arises from the small intestine, most commonly the jejunum or ileum. Other less frequent primary anatomic sites include the duodenum, stomach, colon, or outside the gastrointestinal tract. Type II of this lymphoma may occur sporadically outside the context of celiac disease.

Index terms

  • Enteropathy associated T-cell lymphoma
  • Enteropathy type intestinal T-cell lymphoma
  • Intestinal T-cell lymphoma

Inclusions

  • Enteropathy type intestinal T-cell lymphoma
  • Intestinal T-cell lymphoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A90.0 – T-cell prolymphocytic leukaemia
  • 2A90.1 – T-cell large granular lymphocytic leukaemia
  • 2A90.2 – Chronic lymphoproliferative disorders of NK-cells
  • 2A90.3 – Aggressive NK cell leukaemia
  • 2A90.4 – Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood
  • 2A90.5 – Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
  • 2A90.6 – Extranodal NK/T-cell lymphoma, nasal type
  • 2A90.8 – Hepatosplenic T-cell lymphoma
  • 2A90.9 – Angioimmunoblastic T-cell lymphoma
  • 2A90.A – Anaplastic large cell lymphoma, ALK-positive
  • 2A90.B – Anaplastic large cell lymphoma, ALK-negative
  • 2A90.C – Peripheral T-cell lymphoma, not otherwise specified

Foundation entity

Enteropathy associated T-cell lymphoma – http://id.who.int/icd/entity/958629729

Allowed postcoordination axes

Part of: 2A90: Mature T-cell lymphoma, specified types, nodal or systemic › 02: Neoplasms