Anaplastic large cell lymphoma, ALK-negative

Description

A T-cell peripheral lymphoma morphologically indistinguishable from anaplastic large cell lymphoma, ALK-positive. It is characterised by the absence of the translocation involving the ALK gene and lacks expression of ALK fusion protein.

Index terms

Anaplastic large cell lymphoma, ALK-negative
Breast implant-associated anaplastic large cell lymphoma

Excludes

2B03 – Primary cutaneous CD30-positive T-cell lymphoproliferative disorders

Exclusions from above levels

2E03 – Malignant neoplasm metastasis in bone or bone marrow
http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

2A90.0 – T-cell prolymphocytic leukaemia
2A90.1 – T-cell large granular lymphocytic leukaemia
2A90.2 – Chronic lymphoproliferative disorders of NK-cells
2A90.3 – Aggressive NK cell leukaemia
2A90.4 – Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood
2A90.5 – Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
2A90.6 – Extranodal NK/T-cell lymphoma, nasal type
2A90.7 – Enteropathy associated T-cell lymphoma
2A90.8 – Hepatosplenic T-cell lymphoma
2A90.9 – Angioimmunoblastic T-cell lymphoma
2A90.A – Anaplastic large cell lymphoma, ALK-positive
2A90.C – Peripheral T-cell lymphoma, not otherwise specified

Foundation entity

Anaplastic large cell lymphoma, ALK-negative – http://id.who.int/icd/entity/1179967777

Allowed postcoordination axes

Part of: 2A90: Mature T-cell lymphoma, specified types, nodal or systemic › 02: Neoplasms