2A90.5ICD-11 MMS 2026-01
Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
Description
A peripheral (mature) T-cell neoplasm linked to the human T-cell leukaemia virus type 1 (HTLV-1). Adult T-cell leukaemia/lymphoma is endemic in several regions of the world, in particular Japan, the Caribbean, and parts of Central Africa.
Index terms
- Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
- adult T-cell lymphoma or leukaemia (HTLV-1-associated) without mention of remission
- adult t cell leukaemia lymphoma
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- adult t-cell leukaemia
- adult t-cell leukaemia or lymphoma (HTLV-1 positive)
- adult t-cell leukaemia or lymphoma HTLV-1 - [human t-cell lymphotropic virus type 1 positive]
- adult t-cell lymphoma
- adult t-cell lymphoma or leukaemia (HTLV-1-associated), NOS
- cortical T ALL
- pre-T ALL
- precursor t-cell lymphoblastic leukaemia
- pro-T ALL
- t-cell acute lymphoblastic leukaemia
- Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated in complete remission
- Acute variant of adult T-cell lymphoma or leukaemia
- Chronic variant of adult T-cell lymphoma or leukaemia
- Lymphomatoid variant of adult T-cell lymphoma or leukaemia
- Smouldering variant of adult T-cell lymphoma or leukaemia
Exclusions from above levels
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Sibling codes
2A90.0– T-cell prolymphocytic leukaemia2A90.1– T-cell large granular lymphocytic leukaemia2A90.2– Chronic lymphoproliferative disorders of NK-cells2A90.3– Aggressive NK cell leukaemia2A90.4– Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood2A90.6– Extranodal NK/T-cell lymphoma, nasal type2A90.7– Enteropathy associated T-cell lymphoma2A90.8– Hepatosplenic T-cell lymphoma2A90.9– Angioimmunoblastic T-cell lymphoma2A90.A– Anaplastic large cell lymphoma, ALK-positive2A90.B– Anaplastic large cell lymphoma, ALK-negative2A90.C– Peripheral T-cell lymphoma, not otherwise specified
Foundation entity
Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated – http://id.who.int/icd/entity/1638811270
Allowed postcoordination axes
Part of: 2A90: Mature T-cell lymphoma, specified types, nodal or systemic › 02: Neoplasms