2A90.C

ICD-11 MMS 2026-01

Peripheral T-cell lymphoma, not otherwise specified

Description

A heterogeneous category of nodal and extranodal mature T-cell lymphomas, which do not correspond to any of the specifically defined entities of mature T-cell lymphoma in the current classification.

Index terms

  • Peripheral T-cell lymphoma, not otherwise specified
  • Follicular variant Peripheral T-cell lymphoma
  • Lennert lymphoma
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  • Lymphoepithelioid lymphoma
  • T-zone variant Peripheral T-cell lymphoma
  • mature t-cell lymphoma
  • peripheral t-cell lymphoma - pleomorphic medium and large cell
  • peripheral t-cell lymphoma - pleomorphic small cell
  • peripheral t-cell lymphoma AILD - [angioimmunoblastic lymphadenopathy with dysproteinaemia]
  • peripheral t-cell lymphoma NOS
  • peripheral t-cell lymphoma unspecified

Inclusions

  • Follicular variant Peripheral T-cell lymphoma
  • Lymphoepithelioid lymphoma
  • T-zone variant Peripheral T-cell lymphoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A90.0 – T-cell prolymphocytic leukaemia
  • 2A90.1 – T-cell large granular lymphocytic leukaemia
  • 2A90.2 – Chronic lymphoproliferative disorders of NK-cells
  • 2A90.3 – Aggressive NK cell leukaemia
  • 2A90.4 – Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood
  • 2A90.5 – Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated
  • 2A90.6 – Extranodal NK/T-cell lymphoma, nasal type
  • 2A90.7 – Enteropathy associated T-cell lymphoma
  • 2A90.8 – Hepatosplenic T-cell lymphoma
  • 2A90.9 – Angioimmunoblastic T-cell lymphoma
  • 2A90.A – Anaplastic large cell lymphoma, ALK-positive
  • 2A90.B – Anaplastic large cell lymphoma, ALK-negative

Foundation entity

Peripheral T-cell lymphoma, not otherwise specified – http://id.who.int/icd/entity/855224800

Allowed postcoordination axes

Part of: 2A90: Mature T-cell lymphoma, specified types, nodal or systemic › 02: Neoplasms