4A01.1

ICD-11 MMS 2026-01

Combined immunodeficiencies

Excludes

  • 4A01.00 – autosomal recessive agammaglobulinaemia (Swiss type)

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A01.10 – Severe combined immunodeficiencies
  • 4A01.11 – Major histocompatibility complex class I deficiency
  • 4A01.12 – Major histocompatibility complex class II deficiency
  • 4A01.1Y – Other specified combined immunodeficiencies
  • 4A01.1Z – Combined immunodeficiencies, unspecified

Sibling codes

  • 4A01.0 – Immunodeficiencies with predominantly antibody defects
  • 4A01.2 – Diseases of immune dysregulation
  • 4A01.3 – Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
  • 4A01.Z – Primary immunodeficiencies due to disorders of adaptive immunity, unspecified

Foundation entity

Combined immunodeficiencies – http://id.who.int/icd/entity/1616506198

Part of: 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system