ICD-11 MMS 2026-01
Primary immunodeficiencies due to disorders of adaptive immunity, unspecified
Exclusions from above levels
02 – Neoplasms18 – Complications of pregnancy, childbirth and the puerperium20 – Developmental anomalies
Sibling codes
4A01.0 – Immunodeficiencies with predominantly antibody defects4A01.1 – Combined immunodeficiencies4A01.2 – Diseases of immune dysregulation4A01.3 – Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
Part of: 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system