5C80.1

ICD-11 MMS 2026-01

Hypertriglyceridaemia

Description

A form of hyperlipidaemia characterised by abnormally elevated levels of triglyceride-rich lipoproteins in the blood. It is associated with an elevated risk of cardiovascular morbidity.

Index terms

  • Hypertriglyceridaemia
  • Endogenous hyperglyceridaemia
  • Fredrickson hyperlipoproteinaemia, type 4
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  • Fredrickson hyperlipoproteinemia, type 4
  • Fredrickson type 4 lipidaemia
  • Hyperlipidaemia, group B
  • elevated fasting triglycerides dyslipidaemia
  • endogenous hyperlipemia
  • endogenous hyperlipidaemia
  • essential hyperglyceridaemia
  • essential hypertriglyceridaemia
  • familial hyperglyceridaemia
  • familial hyperprebetalipoproteinaemia
  • group B hyperlipemia
  • hereditary hyperglyceridaemia
  • hyperglyceridaemia
  • prebetalipoproteinemia
  • very-low-density-lipoid-type hyperlipoproteinemia
  • very-low-density-lipoprotein-type
  • very-low-density-lipoprotein-type hyperlipoproteinemia
  • Major hypertriglyceridaemia
  • Hyperlipoproteinaemia type 1
  • Bürger-Grütz syndrome
  • Fredrickson type 1 hyperlipoproteinaemia
  • Hyperlipidaemia type 1
  • endogenous hypertriglyceridaemia
  • familial fat-induced hypertriglyceridaemia
  • familial hyperchylomicronaemia
  • familial lipoprotein lipase deficiency with type I phenotype
  • familial type 1 hyperlipoproteinaemia
  • hepatosplenomegalic lipoidosis
  • hypercholesterinaemic xanthomatosis
  • hyperchylomicronaemia
  • hyperlipoproteinaemia, type 1
  • mixed endogenous hyperglyceridaemia
  • mixed essential hyperglyceridaemia
  • mixed familial hyperglyceridaemia
  • mixed hereditary hyperglyceridaemia
  • mixed hyperglyceridaemia
  • mixed pure hyperglyceridaemia
  • primary hyperchylomicronaemia
  • Familial apolipoprotein C-II deficiency
  • Familial lipoprotein lipase deficiency
  • Fredrickson type 5 hyperlipoproteinaemia
  • Hyperbetalipoproteinaemia hyperchylomicronaemia
  • hyperchylomicronaemia with hyperbetalipoproteinaemia
  • Hyperlipidaemia group D
  • Hyperlipoproteinaemia type 4
  • Familial hypertriglyceridaemia
  • carbohydrate induced hyperlipemia
  • Familial hyperlipoproteinaemia type 4
  • Secondary hyperlipoproteinaemia type 4
  • Hyperlipoproteinaemia type 5
  • Major hyperlipidaemia
  • Familial hyperlipoproteinaemia type 5
  • Secondary hyperlipoproteinaemia type 5
  • Xanthoma in association with primary hypertriglyceridaemia
  • Xanthoma in association with primary chylomicronaemia
  • Xanthoma in association with chylomicron retention disease
  • Hyperprebetalipoproteinaemia
  • VLDL - [very-low-density-lipoprotein-type] hyperlipoproteinaemia

Inclusions

  • Endogenous hyperglyceridaemia
  • Hyperlipidaemia, group B

Exclusions from above levels

  • 5C56.0 – Sphingolipidosis
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
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  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5C80.0 – Hypercholesterolaemia
  • 5C80.2 – Mixed hyperlipidaemia
  • 5C80.3 – Hyperalphalipoproteinaemia
  • 5C80.Y – Other specified hyperlipoproteinaemia
  • 5C80.Z – Hyperlipoproteinaemia, unspecified

Foundation entity

Hypertriglyceridaemia – http://id.who.int/icd/entity/1820945441

Allowed postcoordination axes

Part of: 5C80: Hyperlipoproteinaemia › 05: Endocrine, nutritional or metabolic diseases