5C80.3

ICD-11 MMS 2026-01

Hyperalphalipoproteinaemia

Description

A condition in which high-density lipoprotein is elevated in the blood.

Index terms

  • Hyperalphalipoproteinaemia
  • Hyperalphalipoproteinaemia due to cholesteryl ester transfer protein deficiency
  • CEPT - [cholesterol-ester transfer protein deficiency] deficiency
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  • Cholesterol-ester transfer protein deficiency
  • Familial hyperalphalipoproteinaemia
  • Hyperlipidaemia due to cubilin deficiency

Exclusions from above levels

  • 5C56.0 – Sphingolipidosis
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
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  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5C80.0 – Hypercholesterolaemia
  • 5C80.1 – Hypertriglyceridaemia
  • 5C80.2 – Mixed hyperlipidaemia
  • 5C80.Y – Other specified hyperlipoproteinaemia
  • 5C80.Z – Hyperlipoproteinaemia, unspecified

Foundation entity

Hyperalphalipoproteinaemia – http://id.who.int/icd/entity/1599779547

Part of: 5C80: Hyperlipoproteinaemia › 05: Endocrine, nutritional or metabolic diseases