5C80.2

ICD-11 MMS 2026-01

Mixed hyperlipidaemia

Description

Elevated levels of both LDL cholesterol and triglycerides in the blood

Index terms

  • Mixed hyperlipidaemia
  • Hyperbetalipoproteinaemia with prebetalipoproteinaemia
  • Hypercholesterolaemia with endogenous hyperglyceridaemia
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  • Hyperlipidaemia, group C
  • familial hyperbetalipoproteinaemia and hyperprebetalipoproteinaemia
  • familial hypercholesterolaemia with hyperlipaemia
  • mixed hyperlipemia
  • prebetalipoproteinemia hyperbetalipoproteinaemia
  • remnant hyperlipoproteinemia
  • Hyperlipidaemia type 3
  • Broad beta disease
  • Broad- or floating-betalipoproteinaemia
  • Broad-betalipoproteinaemia
  • Familial type 3 hyperlipoproteinaemia
  • Fredrickson type 3 hyperlipoproteinaemia
  • Hyperlipoproteinaemia type 3
  • Remnant hyperlipidaemia
  • broad-beta lipoproteinemia
  • floating beta disease
  • floating-beta lipoproteinemia
  • Hyperlipidaemia type 3 - Apolipoprotein E deficiency
  • apolipoprotein E deficiency
  • Hyperlipidaemia type 3 - familial defective apolipoprotein B
  • Hyperlipidaemia type 3 - familial dysbetalipoproteinaemia
  • Familial dysbetalipoproteinaemia
  • dysbetalipoproteinaemia
  • primary dysbetalipoproteinaemia
  • Hyperlipidaemia type 3 - familial dyslipoproteinaemia
  • Secondary hyperlipoproteinaemia type 3
  • Mixed hyperlipidaemia - type IIb hyperlipoproteinaemia
  • Fredrickson type 2B hyperlipoproteinemia
  • familial hyperlipoproteinemia type 2B
  • Familial combined hyperlipidaemia
  • FCH - [familial combined hyperlipidaemia]
  • hyperapobetalipoproteinaemia
  • Secondary combined hyperlipidaemia
  • Mixed hyperlipidaemia due to hepatic triglyceride lipase deficiency
  • Xanthoma in association with primary combined hyperlipidaemia
  • Xanthoma in association with secondary hyperlipidaemia

Inclusions

  • Hyperbetalipoproteinaemia with prebetalipoproteinaemia
  • Hypercholesterolaemia with endogenous hyperglyceridaemia
  • Hyperlipidaemia, group C

Excludes

  • 5C52.11 – cerebrotendinous cholesterosis [van Bogaert-Scherer-Epstein]

Exclusions from above levels

  • 5C56.0 – Sphingolipidosis
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
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  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5C80.0 – Hypercholesterolaemia
  • 5C80.1 – Hypertriglyceridaemia
  • 5C80.3 – Hyperalphalipoproteinaemia
  • 5C80.Y – Other specified hyperlipoproteinaemia
  • 5C80.Z – Hyperlipoproteinaemia, unspecified

Foundation entity

Mixed hyperlipidaemia – http://id.who.int/icd/entity/405028062

Allowed postcoordination axes

Part of: 5C80: Hyperlipoproteinaemia › 05: Endocrine, nutritional or metabolic diseases