5D00.2Y

ICD-11 MMS 2026-01

Other specified hereditary amyloidosis

Exclusions from above levels

  • 6D80 – Dementia due to Alzheimer disease
  • 2B31.2 – histiocytosis X (chronic)
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
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  • 5A71.01 – Congenital adrenal hyperplasia
  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5D00.20 – Hereditary ATTR amyloidosis
  • 5D00.21 – Non-neuropathic heredofamilial amyloidosis
  • 5D00.2Z – Hereditary amyloidosis, unspecified

Foundation entity

Hereditary amyloidosis – http://id.who.int/icd/entity/1152878652

Allowed postcoordination axes

Part of: 5D00.2: Hereditary amyloidosis › 5D00: Amyloidosis › 05: Endocrine, nutritional or metabolic diseases