Non-neuropathic heredofamilial amyloidosis

Description

This is an amyloidosis (the formation of insoluble proteins, or amyloids) of inherited origin that does not affect the peripheral nerves. The most common sites of deposits are associated with the kidney and heart.

Index terms

Non-neuropathic heredofamilial amyloidosis
Cardiac non-neuropathic heredofamilial amyloidosis
Cerebral non-neuropathic heredofamilial amyloidosis angiopathy

Exclusions from above levels

6D80 – Dementia due to Alzheimer disease
2B31.2 – histiocytosis X (chronic)
3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency

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5A71.01 – Congenital adrenal hyperplasia
5A81.1 – 5-alpha-reductase deficiency
LD28.01 – Marfan syndrome
LD28.1 – Ehlers-Danlos syndrome
LD2A.4 – androgen resistance syndrome
18 – Pregnancy, childbirth or the puerperium
http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

5D00.20 – Hereditary ATTR amyloidosis
5D00.2Y – Other specified hereditary amyloidosis
5D00.2Z – Hereditary amyloidosis, unspecified

Foundation entity

Non-neuropathic heredofamilial amyloidosis – http://id.who.int/icd/entity/1431377239

Allowed postcoordination axes

Part of: 5D00.2: Hereditary amyloidosis › 5D00: Amyloidosis › 05: Endocrine, nutritional or metabolic diseases