8C75

ICD-11 MMS 2026-01

Distal myopathies

Description

Distal myopathies are heterogeneous group of myopathies characterised clinically by progressive weakness and atrophy starting in distal muscles and progressing to proximal ones, and histologically by nonspecific myopathic features on muscle biopsy.

Index terms

  • Distal myopathies
  • Distal muscular dystrophy
  • Distal myopathy with anterior tibial onset
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  • Markesbery-Griggs distal myopathy
  • Tibial muscular dystrophy
  • Distal myopathy with early respiratory muscle involvement
  • Distal myopathy with posterior leg or anterior hand involvement
  • Distal myopathy with vocal cord weakness
  • Distal myopathy with rimmed vacuoles
  • Nonaka myopathy
  • Welander distal myopathy
  • WDM – [Welander distal myopathy]
  • Laing distal myopathy
  • Distal myopathy, Miyoshi type
  • Tibial muscular dystrophy, Udd type
  • Certain specified rare distal myopathy

Exclusions from above levels

  • http://id.who.int/icd/entity/155258022 – Metabolic disorders
  • LD26.41 – Arthrogryposis multiplex congenita
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8C70 – Muscular dystrophy
  • 8C71 – Myotonic disorders
  • 8C72 – Congenital myopathies
  • 8C73 – Mitochondrial myopathies
  • 8C74 – Periodic paralyses or disorders of muscle membrane excitability
  • 8C76 – Myofibrillar myopathy
  • 8C77 – Ocular myopathy
  • 8C78 – Malignant hyperthermia or hyperpyrexia
  • 8C7Y – Other specified primary disorders of muscles
  • 8C7Z – Primary disorders of muscles, unspecified

Foundation entity

Distal myopathies – http://id.who.int/icd/entity/596283352

Part of: 08: Diseases of the nervous system