CB03.0ICD-11 MMS 2026-01
Acute interstitial pneumonitis
Description
Acute interstitial pneumonia (pneumonitis), also referred to as Hamman-Rich syndrome, is a rapidly progressive and histologically distinct form of idiopathic interstitial pneumonia (pneumonitis).
Index terms
- Acute interstitial pneumonitis
- Acute interstitial pneumonia
- Hamman-Rich syndrome
Exclusions from above levels
Sibling codes
CB03.1– Combined pulmonary fibrosis and emphysema syndromeCB03.2– Cryptogenic organizing pneumonitisCB03.3– Desquamative interstitial pneumonitisCB03.4– Idiopathic pulmonary fibrosisCB03.5– Lymphoid interstitial pneumoniaCB03.6– Respiratory bronchiolitis - interstitial lung diseaseCB03.Y– Other specified idiopathic interstitial pneumonitisCB03.Z– Idiopathic interstitial pneumonitis, unspecified
Foundation entity
Acute interstitial pneumonitis – http://id.who.int/icd/entity/2116884221
Allowed postcoordination axes
Part of: CB03: Idiopathic interstitial pneumonitis › 12: Diseases of the respiratory system