CB03.5

ICD-11 MMS 2026-01

Lymphoid interstitial pneumonia

Description

This refers to several conditions in which lymphocytes are produced in excessive quantities. They typically occur in patients who have compromised immune systems. They are sometimes equated with "immunoproliferative disorders", but technically lymphoproliferative disorders are a subset of immunoproliferative disorders, along with hypergammaglobulinemia and paraproteinaemias.

Index terms

  • Lymphoid interstitial pneumonia
  • Lymphocytic interstitial pneumonia

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CB03.0 – Acute interstitial pneumonitis
  • CB03.1 – Combined pulmonary fibrosis and emphysema syndrome
  • CB03.2 – Cryptogenic organizing pneumonitis
  • CB03.3 – Desquamative interstitial pneumonitis
  • CB03.4 – Idiopathic pulmonary fibrosis
  • CB03.6 – Respiratory bronchiolitis - interstitial lung disease
  • CB03.Y – Other specified idiopathic interstitial pneumonitis
  • CB03.Z – Idiopathic interstitial pneumonitis, unspecified

Foundation entity

Lymphoid interstitial pneumonia – http://id.who.int/icd/entity/1140418798

Part of: CB03: Idiopathic interstitial pneumonitis › 12: Diseases of the respiratory system