CB03.5ICD-11 MMS 2026-01
Lymphoid interstitial pneumonia
Description
This refers to several conditions in which lymphocytes are produced in excessive quantities. They typically occur in patients who have compromised immune systems. They are sometimes equated with "immunoproliferative disorders", but technically lymphoproliferative disorders are a subset of immunoproliferative disorders, along with hypergammaglobulinemia and paraproteinaemias.
Index terms
- Lymphoid interstitial pneumonia
- Lymphocytic interstitial pneumonia
Exclusions from above levels
Sibling codes
CB03.0– Acute interstitial pneumonitisCB03.1– Combined pulmonary fibrosis and emphysema syndromeCB03.2– Cryptogenic organizing pneumonitisCB03.3– Desquamative interstitial pneumonitisCB03.4– Idiopathic pulmonary fibrosisCB03.6– Respiratory bronchiolitis - interstitial lung diseaseCB03.Y– Other specified idiopathic interstitial pneumonitisCB03.Z– Idiopathic interstitial pneumonitis, unspecified
Foundation entity
Lymphoid interstitial pneumonia – http://id.who.int/icd/entity/1140418798
Part of: CB03: Idiopathic interstitial pneumonitis › 12: Diseases of the respiratory system