CB03.2

ICD-11 MMS 2026-01

Cryptogenic organizing pneumonitis

Description

Cryptogenic organizing pneumonia (pneumonitis) (COP) or bronchiolitis obliterans with organizing pneumonia (pneumonitis) (BOOP) is an inflammatory, non-infectious lung disease with distinctive clinical, radiological and pathological features, and that responds to corticosteroid therapy.

Index terms

  • Cryptogenic organizing pneumonitis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CB03.0 – Acute interstitial pneumonitis
  • CB03.1 – Combined pulmonary fibrosis and emphysema syndrome
  • CB03.3 – Desquamative interstitial pneumonitis
  • CB03.4 – Idiopathic pulmonary fibrosis
  • CB03.5 – Lymphoid interstitial pneumonia
  • CB03.6 – Respiratory bronchiolitis - interstitial lung disease
  • CB03.Y – Other specified idiopathic interstitial pneumonitis
  • CB03.Z – Idiopathic interstitial pneumonitis, unspecified

Foundation entity

Cryptogenic organizing pneumonitis – http://id.who.int/icd/entity/1937662238

Allowed postcoordination axes

Part of: CB03: Idiopathic interstitial pneumonitis › 12: Diseases of the respiratory system