CB03.3ICD-11 MMS 2026-01
Desquamative interstitial pneumonitis
Description
This is a form of idiopathic interstitial pneumonia (pneumonitis) featuring elevated levels of macrophages.
Index terms
- Desquamative interstitial pneumonitis
- Desquamative interstitial pneumonia
Inclusions
- Desquamative interstitial pneumonia
Exclusions from above levels
Sibling codes
CB03.0– Acute interstitial pneumonitisCB03.1– Combined pulmonary fibrosis and emphysema syndromeCB03.2– Cryptogenic organizing pneumonitisCB03.4– Idiopathic pulmonary fibrosisCB03.5– Lymphoid interstitial pneumoniaCB03.6– Respiratory bronchiolitis - interstitial lung diseaseCB03.Y– Other specified idiopathic interstitial pneumonitisCB03.Z– Idiopathic interstitial pneumonitis, unspecified
Foundation entity
Desquamative interstitial pneumonitis – http://id.who.int/icd/entity/1620001155
Allowed postcoordination axes
Part of: CB03: Idiopathic interstitial pneumonitis › 12: Diseases of the respiratory system