2A85.1

ICD-11 MMS 2026-01

Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach

Description

A low grade, indolent B-cell lymphoma, usually associated with Helicobacter pylori infection. Morphologically it is characterised by a dense mucosal atypical lymphocytic (centrocyte-like cell) infiltrate with often prominent lymphoepithelial lesions and plasmacytic differentiation. Some of gastric MALT lymphomas carry the t(11;18)(q21;q21). Such cases are resistant to Helicobacter pylori therapy.

Index terms

  • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
  • MALT - [mucosa associated lymphoid tissue] lymphoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A85.0 – Nodal marginal zone lymphoma
  • 2A85.2 – Extranodal marginal zone B-cell lymphoma, primary site skin
  • 2A85.3 – Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
  • 2A85.4 – Lymphoplasmacytic lymphoma
  • 2A85.5 – Mantle cell lymphoma
  • 2A85.6 – Burkitt lymphoma including Burkitt leukaemia
  • 2A85.Y – Further specified mature B-cell neoplasms or lymphoma

Foundation entity

Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach – http://id.who.int/icd/entity/1168698390

Allowed postcoordination axes

Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms