Burkitt lymphoma including Burkitt leukaemia

Description

A highly aggressive lymphoma composed of monomorphic medium-sized B-cells with basophilic cytoplasm and numerous mitotic figures. It is often associated with the presence of Epstein-Barr virus (EBV) and is commonly seen in AIDS patients. Three morphologic variants are recognised: classical Burkitt lymphoma, Burkitt lymphoma with plasmacytoid differentiation, and atypical Burkitt/Burkitt-like lymphoma. All cases express the MYC translocation [t(8;14)].

Index terms

Burkitt lymphoma including Burkitt leukaemia
Burkitt tumour
diffuse small noncleaved malignant Burkitt lymphoma

Show allHide

malignant Burkitt lymphoma
small noncleaved cell Burkitt lymphoma
undifferentiated Burkitt lymphoma
“Burkitt-like” lymphoma
Mature B-cell leukaemia Burkitt-type
Burkitt cell leukaemia
Burkitt type acute lymphoblastic leukaemia
mature B-cell leukaemia Burkitt-type without mention of remission
Mature B-cell leukaemia Burkitt-type in complete remission

Inclusions

“Burkitt-like” lymphoma

Exclusions from above levels

2E03 – Malignant neoplasm metastasis in bone or bone marrow
http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

2A85.0 – Nodal marginal zone lymphoma
2A85.1 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
2A85.2 – Extranodal marginal zone B-cell lymphoma, primary site skin
2A85.3 – Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
2A85.4 – Lymphoplasmacytic lymphoma
2A85.5 – Mantle cell lymphoma
2A85.Y – Further specified mature B-cell neoplasms or lymphoma

Foundation entity

Burkitt lymphoma including Burkitt leukaemia – http://id.who.int/icd/entity/2100138081

Allowed postcoordination axes

Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms