2A85.5

ICD-11 MMS 2026-01

Mantle cell lymphoma

Description

Mantle cell lymphoma is a rare form of malignant non-Hodgkin lymphoma affecting B lymphocytes in the lymph nodes in a region called the ``mantle zone''. It accounts for 2-10% of lymphomas.

Index terms

  • Mantle cell lymphoma
  • Malignant lymphomatous polyposis
  • Small cell mantle cell lymphoma
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  • cleaved cell lymphoma
  • diffuse non-Hodgkin small cleaved cell lymphoma
  • diffuse small cleaved cell malignant lymphoma
  • diffuse small cleaved-cell lymphoma
  • malignant small cell, noncleaved, diffuse lymphoma
  • malignant undifferentiated cell, non-Burkitt lymphoma
  • small cleaved cell malignant lymphoma
  • small cleaved cell non-Hodgkin lymphoma
  • Blastoid mantle cell lymphoma
  • Classical mantle cell lymphoma
  • Diffuse poorly differentiated lymphocytic malignant lymphoma
  • Marginal zone-like mantle cell lymphoma
  • Pleomorphic mantle cell lymphoma

Inclusions

  • Small cell mantle cell lymphoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A85.0 – Nodal marginal zone lymphoma
  • 2A85.1 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
  • 2A85.2 – Extranodal marginal zone B-cell lymphoma, primary site skin
  • 2A85.3 – Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
  • 2A85.4 – Lymphoplasmacytic lymphoma
  • 2A85.6 – Burkitt lymphoma including Burkitt leukaemia
  • 2A85.Y – Further specified mature B-cell neoplasms or lymphoma

Foundation entity

Mantle cell lymphoma – http://id.who.int/icd/entity/1804127841

Allowed postcoordination axes

Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms