Extranodal marginal zone B-cell lymphoma, primary site skin

Description

A low-grade, extranodal marginal zone B-cell lymphoma of the mucosa-associated lymphoid tissue that arises from the skin. It usually presents with multifocal papular or nodular lesions in the arms or trunk. It rarely disseminates to internal organs or progresses to high grade lymphoma.

Index terms

Extranodal marginal zone B-cell lymphoma, primary site skin
Primary cutaneous marginal zone B-cell lymphoma
SALT - [skin associated lymphoid tissue-related B-cell lymphoma]

Exclusions from above levels

2E03 – Malignant neoplasm metastasis in bone or bone marrow
http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

2A85.0 – Nodal marginal zone lymphoma
2A85.1 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
2A85.3 – Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
2A85.4 – Lymphoplasmacytic lymphoma
2A85.5 – Mantle cell lymphoma
2A85.6 – Burkitt lymphoma including Burkitt leukaemia
2A85.Y – Further specified mature B-cell neoplasms or lymphoma

Foundation entity

Extranodal marginal zone B-cell lymphoma, primary site skin – http://id.who.int/icd/entity/745285555

Allowed postcoordination axes

Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms