2A85.4ICD-11 MMS 2026-01
Lymphoplasmacytic lymphoma
Description
Neoplasm of small B lymphocytes and plasma cells, mostly residing in the bone marrow. Frequently associated with the production of an IgM serum monoclonal protein, then called Waldenström macroglobulinemia (WM).
Index terms
- Lymphoplasmacytic lymphoma
- Waldenström macroglobulinaemia
- Waldenström macroglobulinaemia without mention of remission
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- idiopathic macroglobulinaemia
- primary macroglobulinaemia
- Lymphoplasmacytic lymphoma in complete remission
- Waldenström macroglobulinaemia in complete remission
Inclusions
- Waldenström macroglobulinaemia
- Waldenström macroglobulinaemia without mention of remission
- primary macroglobulinaemia
Excludes
2A82.0– small cell B-cell lymphoma
Exclusions from above levels
2E03– Malignant neoplasm metastasis in bone or bone marrow- http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
- http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland
Sibling codes
2A85.0– Nodal marginal zone lymphoma2A85.1– Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach2A85.2– Extranodal marginal zone B-cell lymphoma, primary site skin2A85.3– Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin2A85.5– Mantle cell lymphoma2A85.6– Burkitt lymphoma including Burkitt leukaemia2A85.Y– Further specified mature B-cell neoplasms or lymphoma
Foundation entity
Lymphoplasmacytic lymphoma – http://id.who.int/icd/entity/2058944823
Allowed postcoordination axes
Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms