2A85.4

ICD-11 MMS 2026-01

Lymphoplasmacytic lymphoma

Description

Neoplasm of small B lymphocytes and plasma cells, mostly residing in the bone marrow. Frequently associated with the production of an IgM serum monoclonal protein, then called Waldenström macroglobulinemia (WM).

Index terms

  • Lymphoplasmacytic lymphoma
  • Waldenström macroglobulinaemia
  • Waldenström macroglobulinaemia without mention of remission
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  • idiopathic macroglobulinaemia
  • primary macroglobulinaemia
  • Lymphoplasmacytic lymphoma in complete remission
  • Waldenström macroglobulinaemia in complete remission

Inclusions

  • Waldenström macroglobulinaemia
  • Waldenström macroglobulinaemia without mention of remission
  • primary macroglobulinaemia

Excludes

  • 2A82.0 – small cell B-cell lymphoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A85.0 – Nodal marginal zone lymphoma
  • 2A85.1 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
  • 2A85.2 – Extranodal marginal zone B-cell lymphoma, primary site skin
  • 2A85.3 – Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
  • 2A85.5 – Mantle cell lymphoma
  • 2A85.6 – Burkitt lymphoma including Burkitt leukaemia
  • 2A85.Y – Further specified mature B-cell neoplasms or lymphoma

Foundation entity

Lymphoplasmacytic lymphoma – http://id.who.int/icd/entity/2058944823

Allowed postcoordination axes

Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms