2B55ICD-11 MMS 2026-01
Rhabdomyosarcoma, primary site
Description
Rhabdomyosarcoma is a malignant soft tissue tumour which develops from cells of striated muscle. It is the most common form of tumour found in children and adolescents.
Coding note from above levels
For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.
Exclusions from above levels
2A01.1– Mesenchymal tumour of meninges2A02.1– Tumours of cranial or paraspinal nerves- http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
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- http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues
Child codes
Sibling codes
2B50– Chondrosarcoma, primary site2B51– Osteosarcoma, primary site2B52– Ewing sarcoma, primary site2B53– Fibroblastic or myofibroblastic tumour, primary site2B54– Undifferentiated pleomorphic sarcoma, primary site2B56– Angiosarcoma, primary site2B57– Kaposi sarcoma, primary site2B58– Leiomyosarcoma, primary site2B59– Liposarcoma, primary site2B5A– Synovial sarcoma, primary site2B5B– Gastrointestinal stromal tumour, primary site2B5C– Endometrial stromal sarcoma, primary site2B5D– Malignant mixed epithelial mesenchymal tumour, primary site2B5E– Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site2B5F– Sarcoma, not elsewhere classified, primary site2B5G– Myosarcoma of uterus, part not specified2B5H– Well differentiated lipomatous tumour, primary site2B5J– Malignant miscellaneous tumours of bone or articular cartilage of other or unspecified sites2B5K– Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites2B5Y– Other specified malignant mesenchymal neoplasms2B5Z– Malignant mesenchymal neoplasm of unspecified type
Foundation entity
Rhabdomyosarcoma, primary site – http://id.who.int/icd/entity/800945476
Allowed postcoordination axes
Part of: 02: Neoplasms