Endometrial stromal sarcoma, primary site

Description

A malignant, infiltrating mesenchymal tumour arising from the uterine corpus, cervix, vagina, and the ovary. Based on its morphologic characteristics, it is classified as either a low grade or an undifferentiated (high grade) stromal sarcoma. The low grade endometrioid stromal sarcoma is characterised by the presence of oval to spindle-shape cells that resemble the cells of the endometrial stroma, without evidence of significant atypia and pleomorphism. Numerous small vessels are also present. The undifferentiated stromal sarcoma is characterised by an aggressive clinical course, the presence of significant cellular atypia, pleomorphism, and high mitotic activity.

Coding note from above levels

For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.

Index terms

Endometrial stromal sarcoma, primary site
Endometrial stromal sarcoma of uterus
endometrial stromal sarcoma isthmus uteri

Exclusions from above levels

2A01.1 – Mesenchymal tumour of meninges
2A02.1 – Tumours of cranial or paraspinal nerves
http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures

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http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues

Sibling codes

2B50 – Chondrosarcoma, primary site
2B51 – Osteosarcoma, primary site
2B52 – Ewing sarcoma, primary site
2B53 – Fibroblastic or myofibroblastic tumour, primary site
2B54 – Undifferentiated pleomorphic sarcoma, primary site
2B55 – Rhabdomyosarcoma, primary site
2B56 – Angiosarcoma, primary site
2B57 – Kaposi sarcoma, primary site
2B58 – Leiomyosarcoma, primary site
2B59 – Liposarcoma, primary site
2B5A – Synovial sarcoma, primary site
2B5B – Gastrointestinal stromal tumour, primary site
2B5D – Malignant mixed epithelial mesenchymal tumour, primary site
2B5E – Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site
2B5F – Sarcoma, not elsewhere classified, primary site
2B5G – Myosarcoma of uterus, part not specified
2B5H – Well differentiated lipomatous tumour, primary site
2B5J – Malignant miscellaneous tumours of bone or articular cartilage of other or unspecified sites
2B5K – Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites
2B5Y – Other specified malignant mesenchymal neoplasms
2B5Z – Malignant mesenchymal neoplasm of unspecified type

Foundation entity

Endometrial stromal sarcoma, primary site – http://id.who.int/icd/entity/990494080

Allowed postcoordination axes

Part of: 02: Neoplasms