8A43.0ICD-11 MMS 2026-01
Neuromyelitis optica aquaporin-4 antibody positive
Description
Neuromyelitis optica (NMO) is an inflammatory demyelinating disease of the central nervous system characterised mainly by attacks of uni- or bilateral optic neuritis (ON) and acute longitudinally extensive (> 3 vertebral segments) myelitis. This form is seropositive for aquaporin-4 antibodies.
Index terms
- Neuromyelitis optica aquaporin-4 antibody positive
- AQP-4 antibody positive optical neuritis
Exclusions from above levels
05– Endocrine, nutritional or metabolic diseases18– Complications of pregnancy, childbirth and the puerperium19– Certain conditions originating in the perinatal period
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22– Injury, poisoning or certain other consequences of external causes
Sibling codes
8A43.1– Neuromyelitis optica aquaporin-4 antibody negative8A43.2– Single transverse myelitis aquaporin-4 antibody positive8A43.3– Recurrent transverse myelitis aquaporin-4 antibody positive8A43.4– Single optic neuritis aquaporin-4 antibody positive8A43.5– Recurrent optic neuritis aquaporin-4 antibody positive8A43.Y– Other specified neuromyelitis optica8A43.Z– Neuromyelitis optica, unspecified
Foundation entity
Neuromyelitis optica aquaporin-4 antibody positive – http://id.who.int/icd/entity/73324466
Part of: 8A43: Neuromyelitis optica › 08: Diseases of the nervous system