8A43

ICD-11 MMS 2026-01

Neuromyelitis optica

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8A43.0 – Neuromyelitis optica aquaporin-4 antibody positive
  • 8A43.1 – Neuromyelitis optica aquaporin-4 antibody negative
  • 8A43.2 – Single transverse myelitis aquaporin-4 antibody positive
  • 8A43.3 – Recurrent transverse myelitis aquaporin-4 antibody positive
  • 8A43.4 – Single optic neuritis aquaporin-4 antibody positive
  • 8A43.5 – Recurrent optic neuritis aquaporin-4 antibody positive
  • 8A43.Y – Other specified neuromyelitis optica
  • 8A43.Z – Neuromyelitis optica, unspecified

Foundation children elsewhere

  • 8A41.1 – Neuromyelitis optica myelin oligodendrocyte glycoprotein antibody-positive

Sibling codes

  • 8A40 – Multiple sclerosis
  • 8A41 – Isolated demyelinating syndromes of the central nervous system
  • 8A42 – Acute disseminated encephalomyelitis
  • 8A44 – Leukodystrophies
  • 8A45 – Secondary white matter disorders
  • 8A46 – Central demyelination of corpus callosum
  • 8A4Y – Other specified multiple sclerosis or other white matter disorders
  • 8A4Z – Multiple sclerosis or other white matter disorders, unspecified

Foundation entity

Neuromyelitis optica – http://id.who.int/icd/entity/744293382

Allowed postcoordination axes

Part of: 08: Diseases of the nervous system