8A43.3ICD-11 MMS 2026-01
Recurrent transverse myelitis aquaporin-4 antibody positive
Description
Two or more episodes of transverse myelitis which is typically longitudinally extensive (>3 vertebral segments) associated with seropositivity for aquaporin-4 antibodies but without sufficient features to fulfill the 2006 NMO diagnostic criteria.
Index terms
- Recurrent transverse myelitis aquaporin-4 antibody positive
- recurrent AQP-4 positive transverse myelitis
Exclusions from above levels
05– Endocrine, nutritional or metabolic diseases18– Complications of pregnancy, childbirth and the puerperium19– Certain conditions originating in the perinatal period
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22– Injury, poisoning or certain other consequences of external causes
Sibling codes
8A43.0– Neuromyelitis optica aquaporin-4 antibody positive8A43.1– Neuromyelitis optica aquaporin-4 antibody negative8A43.2– Single transverse myelitis aquaporin-4 antibody positive8A43.4– Single optic neuritis aquaporin-4 antibody positive8A43.5– Recurrent optic neuritis aquaporin-4 antibody positive8A43.Y– Other specified neuromyelitis optica8A43.Z– Neuromyelitis optica, unspecified
Foundation entity
Recurrent transverse myelitis aquaporin-4 antibody positive – http://id.who.int/icd/entity/1829846416
Part of: 8A43: Neuromyelitis optica › 08: Diseases of the nervous system