CB04.1

ICD-11 MMS 2026-01

Pulmonary lymphatic dysplasia syndromes

Index terms

  • Pulmonary lymphatic dysplasia syndromes
  • Congenital chylothorax

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
Show allHide
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Foundation children elsewhere

  • EE11.1 – Yellow nail syndrome

Sibling codes

  • CB04.0 – Diffuse pulmonary developmental disorders
  • CB04.2 – Disorders of surfactant metabolism
  • CB04.3 – Alveolar or peri-alveolar conditions
  • CB04.4 – Pulmonary capillaritis
  • CB04.5 – Brain-lung-thyroid syndrome
  • CB04.6 – Chronic pneumonitis of infancy
  • CB04.7 – Neuroendocrine cell hyperplasia of infancy
  • CB04.Y – Other specified primary interstitial lung diseases specific to infancy or childhood
  • CB04.Z – Primary interstitial lung diseases specific to infancy or childhood, unspecified

Foundation entity

Pulmonary lymphatic dysplasia syndromes – http://id.who.int/icd/entity/2105358588

Part of: CB04: Primary interstitial lung diseases specific to infancy or childhood › 12: Diseases of the respiratory system