Pulmonary capillaritis

Description

Isolated pauciimmune pulmonary capillaritis is a small vessel vasculitis restricted to the lungs that may induce diffuse alveolar haemorrhage with dyspnoea, anaemia, chest pain, haemoptysis, bilateral and diffuse alveolar infiltrates at chest X-rays, without any underlying systemic disease. ANCA are frequently positive but could be negative.

Index terms

Pulmonary capillaritis
Isolated pulmonary capillaritis
Pulmonary Langerhans cell histiocytosis specific to childhood

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Pulmonary LCH - [Langerhans cell histiocytosis] specific to childhood

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

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19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations and chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

CB04.0 – Diffuse pulmonary developmental disorders
CB04.1 – Pulmonary lymphatic dysplasia syndromes
CB04.2 – Disorders of surfactant metabolism
CB04.3 – Alveolar or peri-alveolar conditions
CB04.5 – Brain-lung-thyroid syndrome
CB04.6 – Chronic pneumonitis of infancy
CB04.7 – Neuroendocrine cell hyperplasia of infancy
CB04.Y – Other specified primary interstitial lung diseases specific to infancy or childhood
CB04.Z – Primary interstitial lung diseases specific to infancy or childhood, unspecified

Foundation entity

Pulmonary capillaritis – http://id.who.int/icd/entity/1610022220

Allowed postcoordination axes

laterality

Part of: CB04: Primary interstitial lung diseases specific to infancy or childhood › 12: Diseases of the respiratory system