CB04.7ICD-11 MMS 2026-01
Neuroendocrine cell hyperplasia of infancy
Description
Neuroendocrine cell hyperplasia of infancy is a non-lethal paediatric form of interstitial lung disease (ILD) characterised by tachypnoea and respiratory distress without respiratory failure.
Index terms
- Neuroendocrine cell hyperplasia of infancy
- NCHI - [Neuroendocrine cell hyperplasia of infancy]
- NEHI - [Neuroendocrine cell hyperplasia of infancy]
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- Persistent tachypnoea of infancy
Exclusions from above levels
Sibling codes
CB04.0– Diffuse pulmonary developmental disordersCB04.1– Pulmonary lymphatic dysplasia syndromesCB04.2– Disorders of surfactant metabolismCB04.3– Alveolar or peri-alveolar conditionsCB04.4– Pulmonary capillaritisCB04.5– Brain-lung-thyroid syndromeCB04.6– Chronic pneumonitis of infancyCB04.Y– Other specified primary interstitial lung diseases specific to infancy or childhoodCB04.Z– Primary interstitial lung diseases specific to infancy or childhood, unspecified
Foundation entity
Neuroendocrine cell hyperplasia of infancy – http://id.who.int/icd/entity/1641999159
Allowed postcoordination axes
Part of: CB04: Primary interstitial lung diseases specific to infancy or childhood › 12: Diseases of the respiratory system