Chronic pneumonitis of infancy

Description

Chronic pneumonitis of infancy is a rare paediatric form of interstitial lung disease (ILD) sharing clinical and radiologic features with other forms of ILD (cough, tachypnoea, and infiltrative opacities on chest imaging) and harbouring specific histological abnormalities including diffuse thickening of alveolar septa, hyperplasia of type 2 alveolar epithelial cells (AEC), and presence of primitive mesenchymal cells within the alveolar septa.

Index terms

Chronic pneumonitis of infancy

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

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19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations and chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

CB04.0 – Diffuse pulmonary developmental disorders
CB04.1 – Pulmonary lymphatic dysplasia syndromes
CB04.2 – Disorders of surfactant metabolism
CB04.3 – Alveolar or peri-alveolar conditions
CB04.4 – Pulmonary capillaritis
CB04.5 – Brain-lung-thyroid syndrome
CB04.7 – Neuroendocrine cell hyperplasia of infancy
CB04.Y – Other specified primary interstitial lung diseases specific to infancy or childhood
CB04.Z – Primary interstitial lung diseases specific to infancy or childhood, unspecified

Foundation entity

Chronic pneumonitis of infancy – http://id.who.int/icd/entity/1821220054

Allowed postcoordination axes

laterality

Part of: CB04: Primary interstitial lung diseases specific to infancy or childhood › 12: Diseases of the respiratory system