3A51.1

ICD-11 MMS 2026-01

Sickle cell disease without crisis

Description

A disorder caused by a HbS mutation in the haemoglobin gene. This disorder is characterised by abnormal rigid sickle-shaped red blood cells decreasing its ability to carry oxygen. This disorder may present with fatigue, shortness of breath, dizziness, headaches, pallor of skin or mucous membranes, and jaundice. This disorder is confirmed by identification of HbS mutation by genetic testing.

Index terms

  • Sickle cell disease without crisis
  • Hb S disease
  • Hb SS disease
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  • Hb-SS disease without crisis
  • HbSS without crisis
  • Herrick anaemia
  • SCA - [sickle cell anaemia]
  • SCD - [sickle cell disease]
  • Sickle-cell anaemia NOS
  • Sickle-cell anaemia without crisis
  • haemoglobin S disease
  • haemoglobin SS disease
  • hereditary haemoglobinopathy disorder homozygous for haemoglobin S
  • sickle cell disease NOS
  • sickle cell disorder
  • sickle cell syndrome
  • sickle-cell disorder NOS
  • sickle-cell haemoglobin disease
  • sickling disorder due to haemoglobin S
  • Sickle cell nephropathy
  • Drepanocythemia
  • drepanocytic anaemia
  • drepanocytosis

Exclusions from above levels

  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A51.0 – Sickle cell trait
  • 3A51.2 – Sickle cell disease with crisis
  • 3A51.3 – Compound heterozygous sickling disorders without crisis
  • 3A51.4 – Compound heterozygous sickling disorders with crisis
  • 3A51.5 – Haemoglobin C disease
  • 3A51.6 – Haemoglobin D disease
  • 3A51.7 – High affinity haemoglobin
  • 3A51.8 – Low affinity haemoglobin
  • 3A51.9 – Haemoglobin O disease
  • 3A51.A – Haemoglobin E disease
  • 3A51.B – Haemoglobin C/beta thalassaemia compound heterozygosity
  • 3A51.Y – Other specified sickle cell disorders or other haemoglobinopathies
  • 3A51.Z – Sickle cell disorders or other haemoglobinopathies, unspecified

Foundation entity

Sickle cell disease without crisis – http://id.who.int/icd/entity/1711513381

Part of: 3A51: Sickle cell disorders or other haemoglobinopathies › 03: Diseases of the blood or blood-forming organs