3A51.4

ICD-11 MMS 2026-01

Compound heterozygous sickling disorders with crisis

Description

Compound heterozygous sickling disorders with crisis may present with acute chest syndrome, splenic sequestration, haemolytic crisis, and pain.

Index terms

  • Compound heterozygous sickling disorders with crisis
  • Sickle cell Hb-C disease with crisis
  • Hb S Hb C disease with crisis
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  • Hb SC disease with crisis
  • Sickle cell Hb-C disease with crisis with acute chest syndrome
  • Sickle cell Hb-C disease with crisis with splenic sequestration
  • Sickle cell Hb-C disease with crisis with fever
  • Sickle cell thalassaemia with crisis
  • sickle-cell beta thalassaemia with crisis
  • thalassaemia Hb S disease
  • thalassaemia Hb S disease with crisis
  • Sickle cell thalassaemia with crisis with acute chest syndrome
  • Sickle cell thalassaemia with crisis with splenic sequestration
  • Sickle cell thalassaemia with crisis with fever
  • Sickle-cell thalassaemia with vaso-occlusive pain

Exclusions from above levels

  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A51.0 – Sickle cell trait
  • 3A51.1 – Sickle cell disease without crisis
  • 3A51.2 – Sickle cell disease with crisis
  • 3A51.3 – Compound heterozygous sickling disorders without crisis
  • 3A51.5 – Haemoglobin C disease
  • 3A51.6 – Haemoglobin D disease
  • 3A51.7 – High affinity haemoglobin
  • 3A51.8 – Low affinity haemoglobin
  • 3A51.9 – Haemoglobin O disease
  • 3A51.A – Haemoglobin E disease
  • 3A51.B – Haemoglobin C/beta thalassaemia compound heterozygosity
  • 3A51.Y – Other specified sickle cell disorders or other haemoglobinopathies
  • 3A51.Z – Sickle cell disorders or other haemoglobinopathies, unspecified

Foundation entity

Compound heterozygous sickling disorders with crisis – http://id.who.int/icd/entity/125581497

Part of: 3A51: Sickle cell disorders or other haemoglobinopathies › 03: Diseases of the blood or blood-forming organs